W Paris March 1 at the age of 22 to a rare POLG genetic disease The prince of Luxembourg died Fryderyk. “My wife and I would like to inform about the death of our son with a heavy heart,” Prince Robert of Luxembourg and Princess Julia of Nassau said on Sunday evening.
“Last Friday, February 28, on 'Rare Diseases' Day, our beloved son invited us to his room to talk to him last. Frederik He found strength And the courage to say goodbye to each of us in turn ” – we read in the funeral entry of the royal family Luxembourg on Instagram.
Luxembourg. Prince Fryderyk is dead. “Dad, are you proud of me?”
“He said goodbye to us, which has been circulating in our family for years. Even in his last moments humor and boundless compassion They forced him to leave us with the last laughter … to all of us cheer up“ – parents reported.
“Fryderyk's last question (…) was: Dad, are you proud of me? (…) The answer was very easy and he heard it so many times … but at that moment he needed to assure that he had brought everything he could, in his own Short and beautiful life And that now maybe go on” – said the father of the deceased.
POLG mitochondrial disease. Prince of Luxembourg with a “exhausted battery”
Fryderyk was diagnosed when he was 14 years old. The young prince was the founder of the POLG Foundation, supporting the study of this hereditary mitochondrial disease resulting from the mutation in the Polg gene.
– It happens subtly, slowly The world is getting smaller And smaller – Prince Fryderyk talked about his illness. – you can compare this disease to defective batterywhich will never be fully charged, is still able to exhaustion And finally he will lose energy someday – explained the son of his son, Prince Robert.
POLG symptoms depend on age. Children under 12 years of age are observed: seizures epilepticcognitive regression, motor disorders, vision lossEating difficulties and liver dysfunctions. Elderly, seizures dominate seizuredisorders coordination i neuropathy peripheral.
The marriage of Robert and Julia was not approved dynastically, which is why their children initially (Szarlotta, Aleksander and the Fryeric) wearing titles Count. In 2004, the Grand Duke of Luxembourg Henryk gave them titles princely.